Indian Journal of Medical Research

CLINICAL IMAGES
Year
: 2014  |  Volume : 139  |  Issue : 3  |  Page : 476-

Poland's anomaly


Mittal Aliza, Kailash Chandra Aggarwal 
 Department of Pediatrics VMMC & Safdarjung Hospital New Delhi 110 029, India

Correspondence Address:
Kailash Chandra Aggarwal
Department of Pediatrics VMMC & Safdarjung Hospital New Delhi 110 029
India




How to cite this article:
Aliza M, Aggarwal KC. Poland's anomaly.Indian J Med Res 2014;139:476-476


How to cite this URL:
Aliza M, Aggarwal KC. Poland's anomaly. Indian J Med Res [serial online] 2014 [cited 2021 Jun 23 ];139:476-476
Available from: https://www.ijmr.org.in/text.asp?2014/139/3/476/132217


Full Text

A seven year old male child presented to the Department of Pediatrics at Vardhman Mahavir Medical College & Safdarjung Hospital, New Delhi, India, in February 2013 with asymmetry of chest wall and drooping of left shoulder since birth [Figure 1]A. Chest X-ray revealed hyperlucent right lung field with hypoplasia of second, third ribs in the form of non-visualised anterior ends as compared to the left side and grade 1 Sprengel's deformity of the right shoulder [Figure 1]B. Sprengel's deformity is congenital elevation of shoulder due to failure of the normal descent of scapula from initial mid-cervical position to final thoracic position. On conventional radiography, there is elevation of the affected scapula with the inferior angle rotated medially; pointing to spine. Grade 1 Sprengel's deformity is very mild. The shoulders are almost at the same level and the deformity cannot be noticed with the clothes on. On magnetic resonance imaging (MRI) absent right sided pectoral muscles were identified [Figure 2]A. Normal imaging of pectoral muscles is depicted [Figure 2]B. The clinical and radiological findings were consistent with Poland's anomaly, a birth defect which is characterized by underdevelopment or absence of pectoralis muscle on one side of the body and (but not always) webbing of the fingers (syndactyly) of the hand. Additional signs on the affected side may include hypoplastic forearm, herniated lungs, strabismus, epicanthus, Simian crease of affected extremity, dextrocardia, diaphragmatic hernia, history of maternal diabetes, microcephaly, encephalocele, vertebral, hepatobiliary and renal anomalies. Currently, the patient is advised physiotherapy exercises, will be followed up till the child reaches 12 years of age and is planned for reconstruction surgery.{Figure 1}{Figure 2}