Indan Journal of Medical Research Indan Journal of Medical Research Indan Journal of Medical Research Indan Journal of Medical Research
  Home About us Editorial board Search Ahead of print Current issue Archives Submit article Instructions Subscribe Contacts Login  
  Home Print this page Email this page Small font sizeDefault font sizeIncrease font size Users Online: 2434       

   Table of Contents      
CLINICAL IMAGES
Year : 2014  |  Volume : 139  |  Issue : 3  |  Page : 476

Poland's anomaly


Department of Pediatrics VMMC & Safdarjung Hospital New Delhi 110 029, India

Date of Web Publication9-May-2014

Correspondence Address:
Kailash Chandra Aggarwal
Department of Pediatrics VMMC & Safdarjung Hospital New Delhi 110 029
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


PMID: 24820847

Rights and PermissionsRights and Permissions

How to cite this article:
Aliza M, Aggarwal KC. Poland's anomaly. Indian J Med Res 2014;139:476

How to cite this URL:
Aliza M, Aggarwal KC. Poland's anomaly. Indian J Med Res [serial online] 2014 [cited 2020 Oct 25];139:476. Available from: https://www.ijmr.org.in/text.asp?2014/139/3/476/132217

A seven year old male child presented to the Department of Pediatrics at Vardhman Mahavir Medical College & Safdarjung Hospital, New Delhi, India, in February 2013 with asymmetry of chest wall and drooping of left shoulder since birth [Figure 1]A. Chest X-ray revealed hyperlucent right lung field with hypoplasia of second, third ribs in the form of non-visualised anterior ends as compared to the left side and grade 1 Sprengel's deformity of the right shoulder [Figure 1]B. Sprengel's deformity is congenital elevation of shoulder due to failure of the normal descent of scapula from initial mid-cervical position to final thoracic position. On conventional radiography, there is elevation of the affected scapula with the inferior angle rotated medially; pointing to spine. Grade 1 Sprengel's deformity is very mild. The shoulders are almost at the same level and the deformity cannot be noticed with the clothes on. On magnetic resonance imaging (MRI) absent right sided pectoral muscles were identified [Figure 2]A. Normal imaging of pectoral muscles is depicted [Figure 2]B. The clinical and radiological findings were consistent with Poland's anomaly, a birth defect which is characterized by underdevelopment or absence of pectoralis muscle on one side of the body and (but not always) webbing of the fingers (syndactyly) of the hand. Additional signs on the affected side may include hypoplastic forearm, herniated lungs, strabismus, epicanthus, Simian crease of affected extremity, dextrocardia, diaphragmatic hernia, history of maternal diabetes, microcephaly, encephalocele, vertebral, hepatobiliary and renal anomalies. Currently, the patient is advised physiotherapy exercises, will be followed up till the child reaches 12 years of age and is planned for reconstruction surgery.
Figure 1: (A). Clinical photograph of the child showing asymmetry of chest wall and drooping of left shoulder. (B). Chest radiograph shows hyperlucent right lung field, hypoplasia of second and third ribs (thin white arrows) as compared to left side ribs and grade 1 Sprengel's deformity (thick white arrows) of right shoulder.

Click here to view
Figure 2: (A). Axial MR image confirming absent right sided pectoralis muscle (thin white arrow) and normal pectoralis muscle on the left side (thick white arrow). (B). Axial MR of normal child showing normal pectoral muscles (thick white arrow).

Click here to view





    Figures

  [Figure 1], [Figure 2]



 

Top
 
 
  Search
 
    Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
    Access Statistics
    Email Alert *
    Add to My List *
* Registration required (free)  

 
  In this article
    Article Figures

 Article Access Statistics
    Viewed675    
    Printed10    
    Emailed0    
    PDF Downloaded255    
    Comments [Add]    

Recommend this journal